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Congenital Pulmonary Lymphangiectasia in a Newborn

PostPosted: Fri Jun 15, 2007 10:34 pm
by patoco
Congenital Pulmonary Lymphangiectasia in a Newborn: A Response to Autologous Blood Therapy.

Neonatology. 2007 Feb

Akcakus M, Koklu E, Bilgin M, Kurtoglu S, Altunay L, Canpolat M, Budak N.
Division of Neonatology, Department of Paediatrics, School of Medicine, Erciyes University, Kayseri, Turkey.

Congenital pulmonary lymphangiectasia is a rare condition that may present antenatally with pleural effusions and hydrops, and the prognosis is reported to be very poor. Treatments for lymphangiectasia have included corticosteroids for patients with primary inflammatory conditions, dietary modifications, surgical resection for isolated lesions, octreotide, antiplasmin therapy and fibrin glue pleurodesis. However, there is no experience with pleurodesis by autologous blood therapy in the literature. We present a newborn with primary pulmonary lymphangiectasis who developed progressively profuse chylous pleural effusions after enteral full feeding from the 8th day of life and improved with pleurodesis by autologous blood therapy. Copyright (c) 2007 S. Karger AG, Basel.

PMID: 17568156 [PubMed - as supplied by publisher] ... d_RVDocSum


Pat O'Connor
Lymphedema People